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J R Mendell Selected Research

J R Mendell Research Topics

Disease

3Limb-Girdle Muscular Dystrophies (Limb-Girdle Muscular Dystrophy)
07/2008 - 12/2000
2Duchenne Muscular Dystrophy (Muscular Dystrophy, Becker)
05/2007 - 02/2006
2Muscular Dystrophies (Muscular Dystrophy)
02/2006 - 12/2000
2Painful Neuropathy
12/2001 - 04/2001
2Chronic Inflammatory Demyelinating Polyradiculoneuropathy (CIDP)
02/2001 - 02/2001
1Fibrosis (Cirrhosis)
01/2016
1type 2E Limb-girdle muscular dystrophy
01/2016
1Infections
02/2014
1Sarcoglycanopathies
07/2008
1Scoliosis
05/2007
1Compression Fractures (Compression Fracture)
05/2007
1Bone Fractures (Bone Fracture)
05/2007
1Walker-Warburg Syndrome
02/2006
1Generalized Epilepsy
02/2006
1Absence Epilepsy (Childhood Absence Epilepsy)
02/2006
1Inclusion Body Myositis
01/2006
1Myotonia
11/2004
1Chronic Pain
09/2003
1Pain (Aches)
12/2001
1Sleep Initiation and Maintenance Disorders (Insomnia)
10/2001
1Tremor (Tremors)
10/2001
1Muscle Cramp (Cramp)
10/2001
1Atrophy
10/2001
1Emery-Dreifuss Muscular Dystrophy (Scapuloperoneal Muscular Dystrophy)
09/2001
1Neuropathy ataxia and retinitis pigmentosa
07/2001
1Intellectual Disability (Idiocy)
04/2001
1Hypertension (High Blood Pressure)
04/2001
1Seizures (Absence Seizure)
04/2001
1Cerebellar Ataxia (Dysmetria)
04/2001
1Mitochondrial Encephalomyopathies (Mitochondrial Encephalomyopathy)
04/2001
1Ataxia (Dyssynergia)
04/2001
1Recurrent Myoglobinuria
04/2001
1Neurologic Manifestations (Neurological Manifestations)
02/2001
1type 2C Limb-girdle muscular dystrophy
12/2000
1Muscular Diseases (Myopathy)
12/2000
1Failure to Thrive
12/2000
1Cytochrome-c Oxidase Deficiency
12/2000
1Hepatomegaly
12/2000
1Pancreatitis
12/2000
1Vomiting
12/2000
1Vasculitis (Vasculitides)
09/2000
1Lactic Acidosis
07/2000
1Hypokalemic Periodic Paralysis (Periodic Paralysis, Hypokalemic)
01/2000
1Paralysis (Palsy)
01/2000

Drug/Important Bio-Agent (IBA)

3Sarcoglycans (beta Sarcoglycan)IBA
01/2016 - 12/2000
3Adrenal Cortex Hormones (Corticosteroids)IBA
05/2007 - 02/2001
2Proteins (Proteins, Gene)FDA Link
01/2016 - 02/2001
2PotassiumIBA
11/2004 - 01/2000
2Intravenous Immunoglobulins (IVIG)FDA Link
02/2001 - 02/2001
1CollagenIBA
01/2016
1Dystrophin-Associated ProteinsIBA
01/2016
1AntibodiesIBA
02/2014
1SteroidsIBA
05/2007
1Laminin (Merosin)IBA
02/2006
1CalpainIBA
02/2006
1DystrophinIBA
02/2006
1Etanercept (Enbrel)FDA Link
01/2006
1Acetazolamide (Diamox)FDA LinkGeneric
11/2004
1gamma-Aminobutyric Acid (GABA)IBA
12/2001
1Tiagabine (Gabitril)FDA Link
12/2001
1Albuterol (Salbutamol)FDA LinkGeneric
10/2001
1Anabolic AgentsIBA
10/2001
1Lamin Type A (Lamin A)IBA
09/2001
1Adenosine Triphosphatases (ATPase)IBA
07/2001
1LipidsIBA
04/2001
1coenzyme Q10 (CoQ10)IBA
04/2001
1Cholinergic Agents (Cholinergics)IBA
04/2001
16-chloropenicillanic acid S-sulfoxideIBA
04/2001
1Mitochondrial DNA (mtDNA)IBA
12/2000
1phytobacteriomycin (PBM)IBA
09/2000
1EnzymesIBA
07/2000
1Carbonic Anhydrase InhibitorsIBA
01/2000
1Dichlorphenamide (Daranide)FDA Link
01/2000

Therapy/Procedure

1Plasmapheresis
02/2014
1Therapeutics
09/2003
1Plasma Exchange
02/2001